Non disponible en dehors du Royaume-Uni et de l'Irlande

Biochem/physiol Actions

Galactose-1-phosphate uridyltransferase (GALT) facilitates the simultaneous conversion of uridine diphosphoglucose (UDP-glucose) and galactose-1-phosphate (gal-1P) to uridine diphosphogalactose (UDP-galactose) and glucose-1-phosphate. Classic Galactosemia (CG) is an inherited metabolic condition caused by deficiency of GALT activity.

Packaging

20, 50 units in glass bottle

Physical form

Contains buffer salts as citrate and reduced glutathione

Unit Definition

One unit will form 1.0 µmole of glucose 1-phosphate from UDP-glucose, galactose 1-phosphate and NADP⁺ per min at pH 8.7 at 25 °C as detected by a coupled system using phosphoglucomutase.